The XY Female: Exploring Care for Adolescent Girls with Complete Androgen Insensitivity Syndrome
Journal article
Davies, K. (2019). The XY Female: Exploring Care for Adolescent Girls with Complete Androgen Insensitivity Syndrome. Comprehensive Child and Adolescent Nursing. 43 (4), pp. 378-388. https://doi.org/10.1080/24694193.2019.1691677
| Authors | Davies, K. |
|---|---|
| Abstract | © 2019, © 2019 Taylor & Francis. Differences in Sex Development (DSD) encompasses many diagnoses, where the development of chromosomal make-up, gonadal development or anatomical development is atypical. XY, DSD is a classification under the recent international consensus statement, and XY females commonly encapsulate disorders of androgen synthesis and androgen action. Complete Androgen Insensitivity Syndrome (CAIS) is the most common XY, DSD diagnosis, which results in an individual having XY chromosomes, but the person is phenotypically female. This article explores the care and management of children and young people with a DSD and focuses on the diagnosis of CAIS in adolescence. Medical and surgical management is discussed, alongside sexual function, gender identity and the psychological impact of the diagnosis. The involvement of the multidisciplinary team is stressed, together with an emphasis on the investment that is needed in psychological and nursing support for girls with CAIS, and their families. |
| Keywords | Pediatrics |
| Year | 2019 |
| Journal | Comprehensive Child and Adolescent Nursing |
| Journal citation | 43 (4), pp. 378-388 |
| Publisher | Informa UK Limited |
| ISSN | 2469-4193 |
| 2469-4207 | |
| Digital Object Identifier (DOI) | https://doi.org/10.1080/24694193.2019.1691677 |
| Publication dates | |
| Online | 21 Nov 2019 |
| 01 Oct 2020 | |
| Publication process dates | |
| Accepted | 07 Nov 2019 |
| Deposited | 10 Sep 2020 |
| Page range | 1-11 |
| File | License File Access Level Open |
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